苯丙酮尿症患儿血苯丙氨酸浓度宜维持在A、0.12~0.48mmol(2~8mg/

资格题库2022-08-02  16

问题 苯丙酮尿症患儿血苯丙氨酸浓度宜维持在A、0.12~0.48mmol(2~8mg/dl)B、0.12~0.6mmol(2~10mg/dl)C、0.06~0.12mmol(1~2mg/dl)D、0.06~0.02mmol(1~4mg/dl)E、0.12~0.24mmol(2~4mg/dl)

选项 A、0.12~0.48mmol(2~8mg/dl)
B、0.12~0.6mmol(2~10mg/dl)
C、0.06~0.12mmol(1~2mg/dl)
D、0.06~0.02mmol(1~4mg/dl)
E、0.12~0.24mmol(2~4mg/dl)

答案 B

解析 每天苯丙氨酸按30~50mg/kg供给,以能维持血苯丙氨酸浓度在0.12~0.6mmol/L(2~10mg/dl)为宜。
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